Citation, DOI and article data
Tricuspid atresia is a cyanotic congenital cardiac anomaly which is characterized by agenesis of the tricuspid valve and right ventricular inlet. There is almost always an obligatory intra-atrial connection through either an ASD or patent foramen ovale (PFO) in order for circulation to be complete 5. A small VSD is often also present. In a proportion of cases, tricuspid atresia may also be associated with transposition of great arteries (TGA).
- giant (>5 mm) P waves 6
- with peaked morphology in lead II
- exaggeration of right atrial enlargement morphology
- referred to as "Himalayan P waves"
- extreme axis deviation
- high left ventricular voltage (HLVV)
- left ventricular hypertrophy voltage criteria
It results from an unequal atrioventricular canal division and the right ventricle is typically very hypoplastic.
Recognized extra-cardiac associations include:
Chest radiographic features may vary depending on the presence and extent of a VSD or TGA. May demonstrate decreased pulmonary vascularity (i.e. oligaemic appearance). Cardiac size may be normal or enlarged.
Usually the 1st line imaging modality in utero. It allows direct visualization of the anomaly.
CT and MRI
Allows direct visualization of the anomaly and may typically show a fatty and/or muscular separation of the right atrium from the right ventricle. Cine MRI can offer functional information in addition to anatomy.
- 1. Fletcher BD, Jacobstein MD, Abramowsky CR et-al. Right atrioventricular valve atresia: anatomic evaluation with MR imaging. AJR Am J Roentgenol. 1987;148 (4): 671-4. AJR Am J Roentgenol (abstract) - Pubmed citation
- 2. Goo HW, Park IS, Ko JK et-al. CT of congenital heart disease: normal anatomy and typical pathologic conditions. Radiographics. 2003;23 Spec No : S147-65. doi:10.1148/rg.23si035501 - Pubmed citation
- 3. Brown DL, Emerson DS, Cartier MS et-al. Congenital cardiac anomalies: prenatal sonographic diagnosis. AJR Am J Roentgenol. 1989;153 (1): 109-14. AJR Am J Roentgenol (citation) - Pubmed citation
- 4. Cook AL, Hurwitz LM, Valente AM et-al. Right heart dilatation in adults: congenital causes. AJR Am J Roentgenol. 2007;189 (3): 592-601. doi:10.2214/AJR.07.2420 - Pubmed citation
- 5. Siegel MJ, Bhalla S, Gutierrez FR et-al. MDCT of postoperative anatomy and complications in adults with cyanotic heart disease. AJR Am J Roentgenol. 2005;184 (1): 241-7. AJR Am J Roentgenol (full text) - Pubmed citation
- 6. Davutoglu V, Kilinc M, Dinckal MH. Himalayan P waves in a patient with combined tricuspid and pulmonic stenosis. (2003) Heart (British Cardiac Society). 89 (10): 1216. Pubmed