Rastelli procedure

Dr Henry Knipe and Dr Vincent Tatco et al.

The Rastelli procedure is a surgical procedure to correct certain combinations of cardiovascular defects in patients with cyanotic congenital heart disease.

The operation is based on a redirection of ventricular outflows using an intracardiac baffle that tunnels the left ventricle to the aorta and an external valved conduit that connects the right ventricle and the pulmonary trunk 1-4.    

Most frequent indications include:

A patch (Gore-Tex) is used to direct oxygenated blood from the left ventricle to the aorta. The patch also closes the VSD.  The pulmonary valve is surgically closed and an artificial conduit and valve are constructed from the right ventricle to the pulmonary bifurcations, allowing deoxygenated blood to travel to the lungs for reoxygenation 1-4.

While the early surgical mortality of the Rastelli is acceptable at approximately 5%, questions have been raised about long-term results 5. LVOT and right-sided conduit obstruction can require percutaneous intervention with stent placement or repeat surgery. Nearly 50% of patients who underwent the Rastelli procedure either needed cardiac transplantation or died 20 years after the procedure 2,5.

Complications of the Rastelli procedure include 3:

  • extra-cardiac conduit stenosis (with or without regurgitation), calcification, kinking and aneurysm
  • tunnel patch from the left ventricle to the aortic valve may be complicated by leakage, obstruction, stenosis, or aneurysm
  • branch pulmonary artery stenosis
  • biventricular dysfunction

The procedure was conceived by Gian Carlo Rastelli as a surgical repair for children born with TGA, VSD, and pulmonary stenosis 1. It was first successfully performed by Dr. Robert Wallace at the Mayo Clinic on July 26, 1968 1,6.

Congenital heart disease

There is more than one way to present the variety of congenital heart diseases. Whichever way they are categorized, it is helpful to have a working understanding of normal and fetal circulation, as well as an understanding of the segmental approach to imaging in congenital heart disease.

Article information

rID: 42339
Synonyms or Alternate Spellings:
  • Rastelli operation

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Cases and figures

  • Case 1
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  • Case 2: treating DORV and pulmonary hypoplasia
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