Congenital aortic stenosis
Citation, DOI and article data
Congenital aortic stenosis broadly refers to a congenital narrowing of the aortic lumen. Although the term can mean narrowing at any point, it often relates to a narrowing of the aortic valve. As a broad group, there can be some overlap with ascending aortic coarctation depending on the definition used.
Depending on location it can be classified into three types:
- supra valvular stenosis
- congenital aortic valve stenosis (commonest)
- subvalvular stenosis
- Williams syndrome: with supra valvular type
- bicuspid aortic valve 2,4
- aortic coarctation
- hypoplastic left heart
- quadricuspid aortic valve 4
Chest radiographs can be normal or may show evidence of cardiomegaly.
May show a high flow jet through the aortic valve or narrowed segment.
CT / MRI
Apart from showing a narrowed valve annulus and/or narrowing cross-sectional aortic segment, it may also show:
- cardiomegaly with left ventricular hypertrophy
- post-stenotic dilated segment of the aortic lumen
In MR imaging, velocity encoded phase-contrast cine sequences can assist in assessing the severity of the stenosis by allowing measurement of blood flow velocities and volumes 2
- 1. Gilkeson RC, Ciancibello L, Zahka K. Pictorial essay. Multidetector CT evaluation of congenital heart disease in pediatric and adult patients. AJR Am J Roentgenol. 2003;180 (4): 973-80. AJR Am J Roentgenol (full text) - Pubmed citation
- 2. Kellenberger CJ, Yoo SJ, Büchel ER. Cardiovascular MR imaging in neonates and infants with congenital heart disease. Radiographics. 27 (1): 5-18. doi:10.1148/rg.271065027 - Pubmed citation
- 3. Sebastià C, Quiroga S, Boyé R et-al. Aortic stenosis: spectrum of diseases depicted at multisection CT. Radiographics. 2003;23 Spec No (suppl 1): S79-91. doi:10.1148/rg.23si035506 - Pubmed citation
- 4. Wiant A, Nyberg E, Gilkeson RC. CT evaluation of congenital heart disease in adults. AJR Am J Roentgenol. 2009;193 (2): 388-96. doi:10.2214/AJR.08.2192 - Pubmed citation